. . . . . . . . . . . . "769074"^^ . . . . . "11365357"^^ . . . . . . . "T\u011B\u017Ek\u00E9 kombinovan\u00E9 imunodeficience (SCID - Severe Combined Immunodeficiency Disease) pat\u0159\u00ED k nejz\u00E1va\u017En\u011Bj\u0161\u00EDm form\u00E1m prim\u00E1rn\u00EDch imunodeficienc\u00ED. Onemocn\u011Bn\u00ED postihuje slo\u017Eky p\u0159irozen\u00E9 i adaptivn\u00ED imunity. V perifern\u00ED krvi prakticky chyb\u00ED T lymfocyty, ale posti\u017Een\u00E9 mohou b\u00FDt i B lymfocyty a NK bu\u0148ky. SCID se projevuje p\u0159edev\u0161\u00EDm b\u011Bhem prvn\u00EDch m\u011Bs\u00EDc\u016F \u017Eivota. Kojenci maj\u00ED zv\u00FD\u0161enou n\u00E1chylnost k infekc\u00EDm, kter\u00E9 maj\u00ED siln\u00FD a recidivuj\u00EDc\u00ED pr\u016Fb\u011Bh. Pacienti jsou citliv\u00ED i na b\u011B\u017En\u00E9 oportunn\u00ED mikroorganismy. Velk\u00FDm nebezpe\u010D\u00EDm je o\u010Dkov\u00E1n\u00ED \u017Eiv\u00FDmi vakc\u00EDnami (BCG vakc\u00EDna), je\u017E m\u016F\u017Ee zp\u016Fsobit v\u00E1\u017En\u00E9 onemocn\u011Bn\u00ED a komplikace. L\u00E9\u010Dba spo\u010D\u00EDv\u00E1 v transplantaci kmenov\u00FDch bun\u011Bk krvetvorby (HSCT). Bez l\u00E9\u010Dby pacienti um\u00EDraj\u00ED do jednoho roku \u017Eivota.Incidence SCID je 1 pacient na 50 000 a\u017E 100 000 porod\u016F."@cs . "61"^^ . . . . . . . "T\u011B\u017Ek\u00E9 kombinovan\u00E9 imunodeficience (SCID - Severe Combined Immunodeficiency Disease) pat\u0159\u00ED k nejz\u00E1va\u017En\u011Bj\u0161\u00EDm form\u00E1m prim\u00E1rn\u00EDch imunodeficienc\u00ED. Onemocn\u011Bn\u00ED postihuje slo\u017Eky p\u0159irozen\u00E9 i adaptivn\u00ED imunity. V perifern\u00ED krvi prakticky chyb\u00ED T lymfocyty, ale posti\u017Een\u00E9 mohou b\u00FDt i B lymfocyty a NK bu\u0148ky. SCID se projevuje p\u0159edev\u0161\u00EDm b\u011Bhem prvn\u00EDch m\u011Bs\u00EDc\u016F \u017Eivota. Kojenci maj\u00ED zv\u00FD\u0161enou n\u00E1chylnost k infekc\u00EDm, kter\u00E9 maj\u00ED siln\u00FD a recidivuj\u00EDc\u00ED pr\u016Fb\u011Bh. Pacienti jsou citliv\u00ED i na b\u011B\u017En\u00E9 oportunn\u00ED mikroorganismy."@cs . . . "5516"^^ . "SCID"@cs . . . . . . . . . . . . "SCID"@cs . . . . . . . . . . .